The Revised International Chapel Hill Consensus Conference nomenclature of vasculitides was formed by experts from 12 different countries in the field of vasculitis as a proposed update to the original 1994 International Chapel Hill Consensus Conference nomenclature of vasculitides. This 2012 update is the most widely used system for describing vasculitides.
Classification
Primary vasculitides
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large vessel vasculitis: affecting predominantly large blood vessels (aorta and its major branches) (see large vessel vasculitides)
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medium vessel vasculitis: affecting predominantly medium blood vessels (main visceral arteries and their branches)
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small vessel vasculitis: affecting predominantly small blood vessels (intraparenchymal arteries, arterioles, capillaries, and venules)
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antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis
eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome)
granulomatosis with polyangiitis (formerly known as Wegener granulomatosis)
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immune complex small vessel vasculitis
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variable vessel vasculitis: affecting no predominant type of vessel and can affect vessels of any size and type
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single-organ vasculitis: affecting vessels of any size in only a single organ
primary central nervous system vasculitis (see central nervous system vasculitides)
isolated aortitis (see aortitis)
others (e.g. idiopathic, pauci-immune pulmonary capillaritis)
Secondary vasculitides
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vasculitis associated with systemic disease
lupus vasculitis
rheumatoid vasculitis (see rheumatoid pulmonary vasculitis)
sarcoid vasculitis
others (e.g. Sneddon syndrome)
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vasculitis associated with probable etiology
hepatitis C virus-associated cryoglobulinaemic vasculitis
hepatitis B virus-associated vasculitis
syphilis-associated aortitis
drug-associated immune complex vasculitis
drug-associated ANCA-associated vasculitis (e.g. hydralazine, propylthiouracil, levamisole 2,3)
cancer-associated vasculitis
others (e.g. varicella zoster virus-associated vasculitis)