This site is targeted at medical and radiology professionals, contains user contributed content, and material that may be confusing to a lay audience. Use of this site implies acceptance of our Terms of Use.

Dyke-Davidoff-Masson syndrome

Dr Yuranga Weerakkody and Dr Mai-Lan Ho et al.

The Dyke-Davidoff-Masson syndrome (DDMS) was initially described as changes in the skull seen on skull X-ray in patients with cerebral hemiatrophy, but is now applied more broadly to cross-sectional imaging also. It is characterised by :

thickening of the skull vault (compensatory)
enlargement of the frontal sinus (also ethmoidal and mastoid air-cells)
elevation of the petrous ridge
ipsilateral falcine displacement
Capillary malformations(are a novel finding for children with Dyke-Davidoff-Masson syndrome)⁶

In some sources it is equated to hemispheric infarction, whereas in other sources any cause of cerebral hemiatrophy are included.

Clinical presentation

seizures
facial asymmetry
contralateral hemiparesis
mental retardation⁷

Etymology

It was initially described by C.G Dyke , L.M Davidoff and C.B Masson in 1933 ⁵

Differential diagnosis

General imaging differential considerations include

hemimegalencephaly
Sturge-Weber syndrome - can also be an association
Rasmussen encephalitis - tends not to have calvarial changes

This article is a stub, which means it needs more content. You can contribute to Radiopaedia.org too. Just register and edit... every little bit helps.