The external acoustic canal (EAC) is a rare location for a cholesteatoma with an estimated incidence around 1.2 per 1,000 new otological patients. The overall incidence rate in one large study was 0.30 per year per 100,000 inhabitants 1. For comparison, the annual incidence of middle ear cholesteatoma is around 9.2 per 100,000.
A distinction from keratosis obliterans has been introduced only in the last few decades. Both mainly consist of epithelial debris in the EAC. The most useful findings confirming an EACC are focal osteonecrosis with or without sequestration and lack of epithelial covering of the bony surface 2. The treatment strategies differ with both conditions 3.
- primary or spontaneous EECC: idiopathic form, the pathogenetic events are unclear (rare)
- secondary EEC: postoperative, postinflammatory, posttraumatic, radiation-induced
- EECC with congenital atresia of the external auditory canal
Schüller, Stenvers, and Mayer views of the petrous bone have been largely replaced by CT.
High-resolution bone window CT is the method of choice to localise the lesion and to demonstrate bony erosions.
Cannot show early involvement of compact bone. Its role in EACC is unknown.
Treatment and prognosis
Small lesions can be treated endoscopically under local anaesthesia, whereas larger lesions need surgery to remove the cholesteatoma and affected bone areas. Grafting of defects may be necessary. Prognosis depends on the extent at the time of diagnosis.
History and etymology
EACC has been first reported by Toynbee in 1850.
General imaging differential considerations include
- 1. Owen HH, Rosborg J, Gaihede M. Cholesteatoma of the external ear canal: etiological factors, symptoms and clinical findings in a series of 48 cases. BMC Ear Nose Throat Disord. 2006;6 : 16. doi:10.1186/1472-6815-6-16 - Free text at pubmed - Pubmed citation
- 2. Heilbrun ME, Salzman KL, Glastonbury CM et-al. External auditory canal cholesteatoma: clinical and imaging spectrum. AJNR Am J Neuroradiol. 2003;24 (4): 751-6. AJNR Am J Neuroradiol (full text) - Pubmed citation
- 3. Persaud RA, Hajioff D, Thevasagayam MS et-al. Keratosis obturans and external ear canal cholesteatoma: how and why we should distinguish between these conditions. Clin Otolaryngol Allied Sci. 2004;29 (6): 577-81. doi:10.1111/j.1365-2273.2004.00898.x - Pubmed citation