Fibrosing colonopathy a condition characterized by progressive submucosal fibrosis, particularly of the proximal colon. It is associated with high dose lipase supplementation used to treat exocrine insufficiency of the pancreas, such as in treatment for cystic fibrosis.
Epidemiology
It is more common in children but has been reported in adults 3. The incidence is thought to have declined from previous decades due to the current use of low dose pancreatic enzyme replacement regimens.
Clinical presentation
abdominal pain
vomiting
symptoms of obstruction
Radiographic features
long or short segment colon stricture, usually on the right
the affected colon may be retracted and shortened
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