Pulmonary sclerosing haemangiomas (PSH), also known as pneumocytomas of the lung, are rare benign neoplasms of the lung.
Typically presents in middle age (30-50 years of age). There is a recognised female predilection.
Most patients are asymptomatic. Symptoms if present will include haemoptysis, cough, chest pain, dyspnea, and pleurisy.
It is a rare benign tumor which is microscopically characterized by four main histological components (solid, papillary, sclerotic, and haemangiomatous) in varying proportions. A thin fibrous pseudocapsule separates it from the adjacent compressed lung parenchyma.
There can be significant size variability where the lesions range from under 1 cm to ~8 cm in diameter, although most are < 3.5 cm.
- they usually tend to present as a solitary, well-defined nodular lesion (oval to rounded shadow).
- they occasionally contain areas of calcification
- may show an air-meniscus sign 4: crescentic radiolucency at the periphery of a lung nodule
- often seen as a well defined intraparechymal nodular mass (often juxta-pleural)
- areas of calcification may be present
- may show a radiolucent zone around the lesion 5
- shows significant but inhomogeneous enhancement 2,8
History and etymology
It was first described by A A Leibow and D S Hubell et.al in 1956 3.
lung cancer: overview
non small-cell lung cancer
- adenosquamous carcinoma
- large cell carcinoma
- primary sarcomatoid carcinoma of lung
- squamous cell carcinoma
- salivary gland type tumours
- pulmonary neuroendocrine tumours
- preinvasive lesions
- benign neoplasms
- pulmonary metastases
- lung cancer screening
- lung cancer staging
- non small-cell lung cancer
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