Uterine agenesis

Uterine agenesis is the extreme of Mullerian duct anomalies (Class I) where there is complete absence of uterine tissue above the vagina. 

Epidemiology

The uterine agenesis-hypoplasia spectrum accounts for ~10-15% of all Müllerian duct anomalies.

Clinical presentation

Clinical presentation is characterised by primary amenorrhoea, with normal hormonal levels guaranteed by fully functional gonads.

Pathology

Complete absence of the Mullerian ducts is termed Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome which includes absence of the vagina as well. 

Associations

Abdominal and pelvic anatomy

Updating… Please wait.
Loadinganimation

Alert_accept

Error Unable to process the form. Check for errors and try again.

Alert_accept Thank you for updating your details.