The World Health Organisation (WHO) Classification of CNS tumours is the most widely accepted system. Latest revision has recently been published (2007) and is available as a complete summary pdf here. The number after the slash refers to biological behaviour, not WHO Grade. A A * refers to a 'new' tumour in the classification.

Tumours of neuroepithelial tissues

Astrocytic tumours

• Pilocytic astrocytoma 9421/11 - WHO grade I
• Pilomyxoid astrocytoma 9425/3* - WHO grade II
• Subependymal giant cell astrocytoma 9384/1 - WHO grade I
• Pleomorphic xanthoastrocytoma 9424/3 - WHO grade II
• Diffuse astrocytoma 9400/3 - WHO grade II
• Fibrillary astrocytoma 9420/3
• Protoplasmic astrocytoma 9410/3
• Gemistocytic astrocytoma 9411/3
• Anaplastic astrocytoma 9401/3 - WHO grade III
• Glioblastoma 9440/3 - WHO grade IV
• Giant cell glioblastoma 9441/3 - WHO grade IV
• Gliosarcoma 9442/3 - WHO grade IV
• Gliomatosis cerebri 9381/3

Oligoastrocytic tumours

• Oligoastrocytoma 9382/3 - WHO grade II
• Anaplastic oligoastrocytoma 9382/3 - WHO grade III

Oligodendroglial tumours

• Oligodendroglioma 9450/3 - WHO grade II
• Anaplastic oligodendroglioma 9451/3 - WHO grade III

Ependymal tumours

• Subependymoma 9383/1 - WHO grade I
• Myxopapillary ependymoma 9394/1 - WHO grade I
• Ependymoma 9391/3 - WHO grade II
• Anaplastic ependymoma 9392/3 - WHO grade III

Choroid plexus tumours

• Choroid plexus papilloma 9390/0 - WHO grade I
• Atypical choroid plexus papilloma 9390/1* - WHO grade II
• Choroid plexus carcinoma 9390/3 - WHO grade III

Other neuroepithelial tumours

• Astroblastoma 9430/3
• Chordoid glioma of the third ventricle 9444/1 - WHO grade II
• Angiocentric glioma 9431/1* - WHO grade I

Neuronal and mixed neuronal-glial tumours

• Dysplastic gangliocytoma of cerebellum - (Lhermitte-Duclos) - 9493/0
• Desmoplastic infantile astrocytoma and ganglioglioma - 9412/1 - WHO grade I
• Dysembryoplastic neuroepithelial tumour - 9413/0 - WHO grade I
• Gangliocytoma - 9492/0 - WHO grade I
• Ganglioglioma - 9505/1 - WHO grade I
• Anaplastic ganglioglioma - 9505/3 - WHO grade III
• Papillary glioneuronal tumor - 9509/1* - WHO grade I
• Rosette-forming glioneuronal tumour of the fourth ventricle - 9509/1* - WHO grade I
• Central neurocytoma - 9506/1 - WHO grade II
• Extraventricular neurocytoma - 9506/1* - WHO grade II
• Cerebellar liponeurocytoma - 9506/1* - WHO grade II
• Paraganglioma of the filum terminale - 8680/1 - WHO grade I

Tumours of the pineal region

• Pineocytoma 9361/1 - WHO grade I / II
• Pineal parenchymal tumour of intermediate differentiation 9362/3 - WHO grade II/III
• Pineoblastoma 9362/3 - WHO grade IV
• Papillary tumour of the pineal region 9395/3* - WHO grade II/III

Embryonal tumours

• Medulloblastoma 9470/3 - WHO grade IV
• CNS primitive neuroectodermal tumours (PNETs) 9473/3 - WHO grade IV
• CNS neuroblastoma 9500/3
• CNS ganglioneuroblastoma 9490/3
• Medulloepithelioma 9501/3
• Ependymoblastoma 9392/3
• Atypical teratoid / rhabdoid tumour 9508/3 - WHO grade IV

Tumours of cranial and paraspinal nerves

• Schwannoma (Neurilemoma, neurinoma) 9560/0 - WHO grade I
• Neurofibroma 9540/0 - WHO grade I
• Perineurioma 9571/0 - WHO grade I / II / III
• Malignant peripheral nerve sheath tumour (MPNST) 9540/3 - WHO grade II / III / IV

Tumours of the meninges

Tumours of meningothelial cells

• Meningioma 9530/0 - WHO grade I
• Atypical meningioma 9539/1 - WHO grade II
• Anaplastic meningioma (malignant) 9530/3 - WHO grade III

Mesenchymal tumours

• Lipoma 8850/0
• Angiolipoma 8861/0
• Hibernoma 8880/0
• Liposarcoma (intracranial) 8850/3
• Solitary fibrous tumour 8815/0
• Fibrosarcoma 8810/3
• Malignant fibrous histiocytoma 8830/3
• Leiomyoma 8890/0
• Leiomyosarcoma 8890/3
• Rhabdomyoma 8900/0
• Rhabdomyosarcoma 8900/3
• Chondroma 9220/0
• Chondrosarcoma 9220/3
• Osteoma 9180/0
• Osteosarcoma 9180/3
• Osteochondroma 9210/0
• Haemangioma 9120/0
• Epithelioid haemangioendothelioma 9133/1
• Haemangiopericytoma (CNS) 9150/1 - WHO grade II
• Angiosarcoma 9120/3
• Kaposi sarcoma 9140/3

Primary melanocytic lesions

• Diffuse melanocytosis 8728/0
• Melanocytoma 8728/1
• Malignant melanoma 8720/3
• Meningeal melanomatosis 8728/3

Other neoplasms related to the meninges

• Haemangioblastoma 9161/1 - WHO grade I

Lymphomas and haemopoietic neoplasma

• Malignant lymphomas 9590/3
• Plasmacytoma 9731/3
• Granulocytic sarcoma 9930/3

Germ cell tumours

• Germinoma (CNS) 9064/3
• Embryonal carcinoma (CNS) 9070/3
• Yolk sac tumour (CNS) 9071/3
• Choriocarcinoma (CNS) 9100/3
• Teratoma (CNS) 9080/1
• Mixed germ cell tumours (CNS) 9085/3

Tumours of the sellar region

• Craniopharyngioma 9350/1 - WHO grade I
• Granular cell tumour 9582/0 - WHO grade I
• Pituicytoma 9432/1* - WHO grade I
• Spindle cell oncocytoma of the adenohypophysis 8291/0* - WHO grade I