Williams-Campbell syndrome is a rare form of congenital cystic bronchiectasis, in which distal bronchial cartilage is defective.
It is thought to result from a deficiency of cartilage formation in the 4th to 6th order bronchi.
- Shows cystic bronchiectatic changes typically involving 4th to 6th order bronchi with preservation of the trachea and main bronchi 2
- 1. HP McAdams and J Erasmus, Chest case of the day. Williams-Campbell syndrome, AJR, Vol. 165, Issue 1, 190-191, July 1, 1995
- 2. Edith M. Marom et.al, Pictorial Essay, Diffuse Abnormalities of the Trachea and Main Bronchi, AJR 2001; 176:713-717
- 3. W. Richard Webb, Radiology of Obstructive Pulmonary Disease, AJR:169, September 1997
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