Patient Data
Age: 15 years
Gender: Male
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MRI of the brain demonstrates increased T2 signal and reduced T1 signal in the white matte of the cerebral hemispheres posteriorly. There is faint enhancement at the anterior margin of the signal abnormality.
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Note how the subcortical u-fibers are spared until later in the disease.
Case Discussion
This case illustrates typical features of adrenoleukodystrophy.