Presentation
Constipation.
Patient Data
Age: 2 years
Gender: Male
From the case:
Hirschsprung disease (short segment type)
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Barium enema findings:
- narrowing of recto-sigmoid segment of intestine
- proximal dilatation of the colon
- 'jejunization' of the descending colon
From the case:
Hirschsprung disease (short segment type)
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Annotated images
- short narrowed segment indicated between the yellow dotted lines; TZ = transition zone
- yellow arrows indicate the small bowel (jejunal) pattern to the descending colon
Case Discussion
Case of short segment Hirschsprung disease
Known cause of obstruction in neonates and up to 5 years of age
Recto-sigmoid ratio is an objective method of assessment
Recto-sigmoid ratio less than 1 is diagnostic for the short segment type