Congenital cystic bronchiectasis
Updates to Article Attributes
Body
was changed:
Congenital cystic bronchiectasis is a rare entity, and as the name suggests is characterised by cystic bronchiectasis found in infancy 1. The term appears to have fallen out of favour, due to variable use in older literature. In most instances of congenital cystic bronchiectasis has what is now referred to as Williams-Campbell syndrome, and is the result of deficiency of cartilage in the bronchial wall. Some authors use the terms synonymously 5.
Some cases may have been manifestations of Mounier-Kuhn syndrome.
Additionally the term was used erroneously in older publications to refer to congenital pulmonary airways malformations (CPAM) 4.
As such it is probably best to avoid the term.
-<p><strong>Congenital cystic bronchiectasis</strong> is a rare entity, and as the name suggests is characterised by cystic <a href="/articles/bronchiectasis" title="Bronchiectasis">bronchiectasis</a> found in infancy <sup>1</sup>. The term appears to have fallen out of favour, due to variable use in older literature. In most instances of congenital cystic bronchiectasis has what is now referred to as <a href="/articles/williams-campbell-syndrome" title="Williams-Campbell syndrome">Williams-Campbell syndrome</a>, and is the result of deficiency of cartilage in the bronchial wall. Some authors use the terms synonymously <sup>5</sup>. </p><p>Some cases may have been manifestations of<a href="/articles/mounier-kuhn-syndrome" title="Mounier-Kuhn syndrome"> Mounier-Kuhn syndrome</a>. <a href="/articles/mounier-kuhn-syndrome" title="Mounier-Kuhn syndrome"></a></p><p>Additionally the term was used erroneously in older publications to refer to <a href="/articles/congenital-cystic-adenomatoid-malformation" title="Congenital Cystic Adenomatoid Malformation (CCAM)">congenital pulmonary airways malformations (CPAM)</a> <sup>4</sup>. </p><p>As such it is probably best to avoid the term. </p>- +<p><strong>Congenital cystic bronchiectasis</strong> is a rare entity, and as the name suggests is characterised by <a title="Cystic bronchiectasis" href="/articles/cystic-bronchiectasis">cystic bronchiectasis</a> found in infancy <sup>1</sup>. The term appears to have fallen out of favour, due to variable use in older literature. In most instances of congenital cystic bronchiectasis has what is now referred to as <a href="/articles/williams-campbell-syndrome">Williams-Campbell syndrome</a>, and is the result of deficiency of cartilage in the bronchial wall. Some authors use the terms synonymously <sup>5</sup>.</p><p>Some cases may have been manifestations of<a href="/articles/mounier-kuhn-syndrome"> Mounier-Kuhn syndrome</a>.</p><p>Additionally the term was used erroneously in older publications to refer to <a href="/articles/congenital-cystic-adenomatoid-malformation">congenital pulmonary airways malformations (CPAM)</a> <sup>4</sup>. </p><p>As such it is probably best to avoid the term.</p>
Unable to process the form. Check for errors and try again.