Airway centered interstitial fibrosis is a rare subtype of pulmonary fibrosis with variable outcomes.
Pathology
It is characterized by fibrosis of the respiratory bronchioles and the peribronchiolar interstitium. It may be triggered by exogenous agents or endogenous autoimmune conditions such as rheumatoid arthritis.
Some of the exogenously triggered precipitants include:
Treatment and prognosis
It is thought to have better survival when compared with idiopathic pulmonary fibrosis.
- 1. Lilian Tiemi Kuranishi, Kevin O Leslie, Rimarcs Gomes Ferreira, Ester Aparecida Ney Coletta, Karin Mueller Storrer, Maria Raquel Soares, Carlos Alberto de Castro Pereira. Airway-centered interstitial fibrosis: etiology, clinical findings and prognosis. (2015) Respiratory Research. 16 (1): 1. doi:10.1186/s12931-015-0213-7 - Pubmed
- 2. Churg A, Myers J, Suarez T, Gaxiola M, Estrada A, Mejia M, Selman M. Airway-centered interstitial fibrosis: a distinct form of aggressive diffuse lung disease. (2004) The American journal of surgical pathology. 28 (1): 62-8. doi:10.1097/00000478-200401000-00006 - Pubmed
- 3. https://erj.ersjournals.com/content/44/Suppl_58/P3500 - to be linked
- 4. https://erj.ersjournals.com/content/40/Suppl_56/P3626 - to be linked
- 5. Kuranishi LT, Leslie KO, Ferreira RG, Coletta EA, Storrer KM, Soares MR, de Castro Pereira CA. Airway-centered interstitial fibrosis: etiology, clinical findings and prognosis. (2015) Respiratory research. 16: 55. doi:10.1186/s12931-015-0213-7 - Pubmed
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