Airway centered interstitial fibrosis is a rare subtype of pulmonary fibrosis with variable outcomes.
Pathology
It is characterized by fibrosis of the respiratory bronchioles and the peribronchiolar interstitium. It may be triggered by exogenous agents or endogenous autoimmune conditions such as rheumatoid arthritis.
Some of the exogenously triggered precipitants include:
Treatment and prognosis
It is thought to have better survival when compared with idiopathic pulmonary fibrosis.
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