Atretic parietal cephalocoele

Atretic parietal cephalocoeles (APC) also known as atretic cephalocele, refers to small subscalp lesions that consist of dura, fibrous tissue, and dysplastic brain tissue.

Common presentation in infants and young children. 

Palpable midline parietal soft tissue mass.

It is thought to represent involuted true cephalocele (meningocele or encephalocele) connected to dura mater via a fibrous stalk. 

Associations

Increased incidence of intracranial anomalies.

  • subgaleal soft  tissue mass with intracranial extension via sharply demarcated calvarial defect (cranium bifidum)
  • CSF tract and vertical falcine vein point to the subcutaneous scalp mass
  • vertically oriented primitive falcine vein
  • fibrous stalk connecting the cephalocele
  • focal fenestration of superior sagittal sinus at the atretic parietal cephalocele
  • prominence of superior cerebellar cistern and suprapineal recess
  • superior peaking of the posterior tentorium
  • spinning top configuration of the tentorial incisura

Imaging differential considerations include

The prognosis of atretic cephalocoeles are generally good.

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Article information

rID: 31190
Section: Pathology
Tag: cases
Synonyms or Alternate Spellings:
  • Atretic cephalocele
  • Atretic parietal cephalocele
  • Atretic parietal cephalocele (APC)
  • Atretic parietal cephalocoele

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