Bat wing 4th ventricle sign refers to the morphology of the fourth ventricle in the Joubert anomaly and related syndromes. The absence of a vermis with apposed cerebellar hemispheres give the fourth ventricle an appearance reminiscent of a bat with its wings outstretched.
It is best demonstrated on axial imaging plane and could be easily missed on sagittal and coronal images 3.
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- 3. Sattam SL. Nahla A A.Yasser RF. Joubert syndrome: accuracy of neuro-radiological indings. Journal of Pediatric Neurology, Vol. 2, No. 1, 2004, pp. 33-37