Bouveret syndrome occurs most commonly in elderly women. The presenting clinical situation is variable and non-specific but often includes nausea, vomiting, and epigastric pain. A history of gallstone disease will only be present in a minority of patients 5. Exemplifying reports of non-specific symptoms and comorbidities include synchronous acute diverticulitis 6 and complicating acute pancreatitis 7, just to name a few.
Plain radiograph and CT
Rigler triad (bowel obstruction, pneumobilia, and an ectopic gallstone) is seen only in a subset of patients. In cases where the offending gallstone is identified, its size (and hence the likelihood of mechanical obstruction) may be underestimated if only the calcified portion of the stone is measured 4.
Treatment and prognosis
Early diagnosis is important because mortality is high, with reported figures ranging between 12-33%.
Endoscopy is preferred as a therapeutic option because removal may be performed with mechanical, electrohydraulic, or laser lithotripsy.
Surgery often is not desirable as the patients are often poor surgical candidates secondary to concomitant illnesses and advanced age.
History and etymology
Named after Léon August Bouveret, French internist (1850-1929) 2, the sign was originally described by him in 1896. However, it was actually originally described by Beaussier in 1770 8.
- a preceding history of gallstone disease will only be present in a minority of cases 5,6
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- 7. Zafar A, Ingham G, Jameel JK. "Bouveret's syndrome" presenting with acute pancreatitis a very rare and challenging variant of gallstone ileus. Int J Surg Case Rep. 2013;4 (5): 528-30. doi:10.1016/j.ijscr.2013.01.017 - Free text at pubmed - Pubmed citation
- 8. Bruni SG, Pickup M, Thorpe D. Bouveret's syndrome-a rare form of gallstone ileus causing death: appearance on post-mortem CT and MRI. (2017) BJR case reports. 3 (3): 20170032. doi:10.1259/bjrcr.20170032 - Pubmed
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