Cardiac fibroma
Updates to Article Attributes
A cardiac fibroma (also known as cardiac fibromatosis, fibrous hamartoma, or fibroelastic hamartoma) represents a collection of fibroblasts interspersed among large amounts of collagen (some authors believe that this tumour is a hamartoma rather than a neoplasm).
Epidemiology
Cardiac fibroma is a tumour that primarily affects children (most cases is detected in infants or in utero). They are the second most common benign primary cardiac tumour in children after cardiac rhabdomyoma and second commonest fetal cardiac tumour 2.
Clinical presentation
Cardiac fibromas are often associated with arrhythmias which can be a presenting feature.
Pathology
Associations
There is an increased prevalence of cardiac fibromas in Gorlin syndrome.
Radiographic features
Cardiac fibromas almost always arise in the ventricles, most commonly in the ventricular septum and left ventricular free wall.They.
Macroscopic appearance
They are well defined, solitary, intramyocardial lesions with smooth margins and usually large, with a mean diameter of about 5~5 cm and may obliterate the ventricular cavity.Unlike. Unlike many primary cardiac tumours, fibromas usually have no foci of cystic change, hemorrhage, or necrosis. Calcification is a common findings.
Associations
There is an increased prevalence of cardiac fibromas in Gorlin syndrome.
Radiographic features
CT
At CT, cardiac fibromas are homogeneous soft-tissue masses that are usually sharply marginated, but also can be infiltrative. Dystrophic calcification is common.
MRI
Because of their dense, fibrous nature, the tumors are usually homogeneous and hypointense on T2-weighted MR images and isointense relative to muscle on T1-weighted images.
Cardiac fibromas often demonstrate little or no contrast material enhancement.
-<p>A<strong> cardiac fibroma</strong> (also known as cardiac fibromatosis, fibrous hamartoma, or fibroelastic hamartoma) represents a collection of fibroblasts interspersed among large amounts of collagen (some authors believe that this tumour is a hamartoma rather than a neoplasm).</p><h4>Epidemiology</h4><p>Cardiac fibroma is a tumour that primarily affects children (most cases is detected in infants or in utero). They are the second most common benign <a href="/articles/primary-cardiac-tumours">primary cardiac tumour</a> in children after cardiac rhabdomyoma and second commonest <a href="/articles/fetal-cardiac-tumours">fetal cardiac tumour</a> <sup>2</sup>.</p><h4>Clinical presentation</h4><p>Cardiac fibromas are often associated with arrhythmias which can be a presenting feature.</p><h4>Pathology</h4><h5>Associations</h5><p>There is an increased prevalence of cardiac fibromas in <a href="/articles/gorlin-goltz-syndrome-1">Gorlin syndrome</a>.</p><h4>Radiographic features</h4><p>Cardiac fibromas almost always arise in the ventricles, most commonly in the ventricular septum and left ventricular free wall.They are well defined, solitary, intramyocardial lesions with smooth margins and usually large, with a mean diameter of about 5 cm and may obliterate the ventricular cavity.Unlike many primary cardiac tumours, fibromas usually have no foci of cystic change, hemorrhage, or necrosis. Calcification is a common findings.</p><h5>CT</h5><p>At CT, cardiac fibromas are homogeneous soft-tissue masses that are usually sharply marginated, but also can be infiltrative. Dystrophic calcification is common.</p><h5>MRI</h5><p>Because of their dense, fibrous nature, the tumors are usually homogeneous and hypointense on T2-weighted MR images and isointense relative to muscle on T1-weighted images.</p><p>Cardiac fibromas often demonstrate little or no contrast material enhancement.</p>- +<p>A<strong> cardiac fibroma</strong> (also known as cardiac fibromatosis, fibrous hamartoma, or fibroelastic hamartoma) represents a collection of fibroblasts interspersed among large amounts of collagen (some authors believe that this tumour is a hamartoma rather than a neoplasm).</p><h4>Epidemiology</h4><p>Cardiac fibroma is a tumour that primarily affects children (most cases is detected in infants or in utero). They are the second most common benign <a href="/articles/primary-cardiac-tumours">primary cardiac tumour</a> in children after cardiac rhabdomyoma and second commonest <a href="/articles/fetal-cardiac-tumours">fetal cardiac tumour</a> <sup>2</sup>.</p><h4>Clinical presentation</h4><p>Cardiac fibromas are often associated with arrhythmias which can be a presenting feature.</p><h4>Pathology</h4><p>Cardiac fibromas almost always arise in the ventricles, most commonly in the ventricular septum and left ventricular free wall.</p><h5>Macroscopic appearance</h5><p>They are well defined, solitary, intramyocardial lesions with smooth margins and usually large, with a mean diameter of ~5 cm and may obliterate the ventricular cavity. Unlike many primary cardiac tumours, fibromas usually have no foci of cystic change, hemorrhage, or necrosis. Calcification is a common findings.</p><h5>Associations</h5><p>There is an increased prevalence of cardiac fibromas in <a href="/articles/gorlin-goltz-syndrome-1">Gorlin syndrome</a>.</p><h4>Radiographic features</h4><h5>CT</h5><p>At CT, cardiac fibromas are homogeneous soft-tissue masses that are usually sharply marginated, but also can be infiltrative. Dystrophic calcification is common.</p><h5>MRI</h5><p>Because of their dense, fibrous nature, the tumors are usually homogeneous and hypointense on T2-weighted MR images and isointense relative to muscle on T1-weighted images.</p><p>Cardiac fibromas often demonstrate little or no contrast material enhancement.</p>