Chiari malformations

Dr Henry Knipe and Dr Jeremy Jones et al.

Chiari malformations are a group of defects associated with congenital caudal 'displacement' of the cerebellum and brainstem.

Initial descriptions were based on autopsy observations. Three types were described, with others added later. Types II and III are likely to be related to each other 1

History and etymology

It was first described by Hans Chiari, Austrian pathologist, (1851-1914) in 1891 3. In this and subsequent papers Chiari also credited Julius Arnold (1835-1915), Professor of Anatomy at Heidelberg, on the grounds of a previous publication of a case believed by Arnold to be of a Chiari II malformation. It appears that this is not actually the case, and as such the term Arnold-Chiari to denote Chiari II malformations is no longer advocated 4

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Article Information

rID: 5781
Section: Pathology
Synonyms or Alternate Spellings:
  • Chiari type malformations

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    Case 1: Chiari I
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    Case 2: Chiari I with syrinx
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    Case 3: Chiari II
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    Case 4: Chiari II
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    Case 5: antenatal
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