Claustrum sign

The claustrum sign refers to the bilateral claustral involvement seen in febrile infection-related epilepsy syndrome (FIRES).

This sign is described on T2 and FLAIR sequences, seen as hyperintensity of both claustra during the acute phase and posterior hypointensity during the chronic phase if a complete recovery is not achieved and atrophy has been established.

The combination of status epilepticus and pleocytosis in the CSF are highly specific for febrile infection-related epilepsy syndrome (FIRES) 1,2.

Article information

rID: 82681
Section: Signs
Synonyms or Alternate Spellings:

ADVERTISEMENT: Supporters see fewer/no ads

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.