Collagen vascular disease related interstitial pneumonitis

Last revised by Craig Hacking on 5 Oct 2022

Collagen vascular disease-related interstitial pneumonitis (CVD-IP) refers to a subgroup of interstitial lung disease that is associated with collagen vascular disease.


Some estimate that up to 15% of patients presenting for evaluation of interstitial lung disease may have an underlying collagen vascular disease 2.

Radiographic features 


The frequency of intrathoracic manifestations and the pattern of abnormality can vary, depending on the type of underlying collagen vascular disease.

The most common patterns described are 3

Honeycombing when present may manifest as either a macrocystic honeycombing, microcystic honeycombing or mixed macrocystic and microcystic honeycombing 1.

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