Congenital aortic stenosis

Congenital aortic stenosis broadly refers to a congenital narrowing of the aortic lumen. Although the term can mean narrowing at any point, it often relates to a narrowing of the aortic valve. As a broad group, there can be some overlap with ascending aortic coarctation depending on the definition used.  

Depending on location it can be classified into three types:

  • supra valvular stenosis
  • congenital aortic valve stenosis (commonest)
  • subvalvular stenosis
Associations
Plain radiograph

Chest radiographs can be normal or may show evidence of cardiomegaly.

Echocardiography

May show a high flow jet through the aortic valve or narrowed segment.

CT / MRI

Apart from showing a narrowed valve annulus and/or narrowing cross-sectional aortic segment it may also show:

  • cardiomegaly with left ventricular hypertrophy
  • post-stenotic dilated segment of the aortic lumen

In MR imaging, velocity encoded phase contrast cine sequences can assist assessing the severity of the stenosis by allowing measurement of blood flow velocities and volumes 2

Share Article

Article Information

rID: 7435
Tag: cases
Synonyms or Alternate Spellings:

Support Radiopaedia and see fewer ads

  • Drag
    Case 1 - supravalvular aortic stenosis
    Drag here to reorder.
  • Updating… Please wait.
    Loadinganimation

    Alert accept

    Error Unable to process the form. Check for errors and try again.

    Alert accept Thank you for updating your details.