Congenital aortic stenosis

Congenital aortic stenosis broadly refers to a congenital narrowing of the aortic lumen. Although the term can mean narrowing at any point, it often relates to a narrowing of the aortic valve. As a broad group, there can be some overlap with ascending aortic coarctation depending on the definition used.  

Depending on location it can be classified into three types:

  • supra valvular stenosis
  • congenital aortic valve stenosis (commonest)
  • subvalvular stenosis

Chest radiographs can be normal or may show evidence of cardiomegaly.

May show a high flow jet through the aortic valve or narrowed segment.

Apart from showing a narrowed valve annulus and/or narrowing cross-sectional aortic segment it may also show:

  • cardiomegaly with left ventricular hypertrophy
  • post-stenotic dilated segment of the aortic lumen

In MR imaging, velocity encoded phase contrast cine sequences can assist assessing the severity of the stenosis by allowing measurement of blood flow velocities and volumes 2

Congenital heart disease

There is more than one way to present the variety of congenital heart diseases. Whichever way they are categorised, it is helpful to have a working understanding of normal and fetal circulation, as well as an understanding of the segmental approach to imaging in congenital heart disease.

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    Case 1 - supravalvular aortic stenosis
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