Congenital megacalyces

Congenital megacalyces is an incidental finding which mimics hydronephrosis. It is a result of underdevelopment of the renal medullary pyramids with resultant enlargement of the calyces. It is more frequently seen in males.

The enlarged calyces predispose to stasis, infection and calculus formation. There is an association with congenital megaureter.

This condition is sometimes differentiated from megapolycalycosis which means "enlarged and numerous calyces." Some have differentiated between "megacalycosis" (large calyces, but normal number of calyces) and "polycalycosis" (greater than normal number of calyces, but normal size). Congenital megacalyces in this scheme would be "megacalycosis." It is unclear how often polycalycosis occurs; this condition is, at most, extremely rare.

Due to the lack of normal medullary pyramids, not only are the calyces enlarged but they lack the normal imprint from the papillae, and the calyces have a flat appearance 1. The renal pelvis is of normal size helping to distinguish megacalyces from hydronephrosis.

In addition to enlargement of the calyces, there is often also polycalycosis (increased number of calyces); they are crowded and multifaceted with a mosaic-like appearance.

Congenital megacalyces usually do not require any treatment unless complicated by calculi or infection which then may require specific management. 

Article information

rID: 6580
Tag: cases, cases
Synonyms or Alternate Spellings:
  • Congenital megacalyectasis
  • Megapolycalycosis
  • Megacalycosis
  • Polycalycosis
  • Puigvert disease
  • Puigvert's disease
  • Congenital megacaliectasis

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