Articles

Cases

Courses

Congenital renal anomalies

Last revised by Arlene Campos ◉ on 14 Feb 2025

Citation, DOI, disclosures and article data

Citation:

Radswiki T, Campos A, Weerakkody Y, et al. Congenital renal anomalies. Reference article, Radiopaedia.org (Accessed on 16 Mar 2025) https://doi.org/10.53347/rID-14854

DOI:

https://doi.org/10.53347/rID-14854

Permalink:

https://radiopaedia.org/articles/14854

rID:

14854

Article created:

31 Aug 2011, The Radswiki ◉

Disclosures:

At the time the article was created The Radswiki had no recorded disclosures.

View The Radswiki's current disclosures

Last revised:

14 Feb 2025, Arlene Campos ◉

Disclosures:

At the time the article was last revised Arlene Campos had no financial relationships to ineligible companies to disclose.

View Arlene Campos's current disclosures

Revisions:

14 times, by 12 contributors - see full revision history and disclosures

Systems:

Urogenital, Paediatrics, Obstetrics

Sections:

Gamuts

Tags:

classification

Synonyms:

Congenital renal disease
Congenital renal abnormalities
Congenital kidney anomalies
Congenital renal anomaly

Congenital renal anomalies comprise of vast spectrum of pathologies and include:

renal agenesis
renal dysgenesis
- congenital renal hypoplasia
congenital megacalyectasis
congenital cystic renal disease
- infantile polycystic renal disease: autosomal recessive polycystic kidney disease (ARPKD): Potter type I
- multicystic dysplastic kidneys: Potter type II
- early onset autosomal dominant polycystic kidney disease (ADPKD): Potter type III
- obstructive cystic renal dysplasia: Potter type IV
obstructive renal disease
- congenital PUJ obstruction
pretumorous conditions
- nephroblastomatosis
renal morphological anomalies / renal fusional anomalies
congenital renal positional anomalies
- pelvic kidney
- fused pelvic kidney
tumors presenting in antenatal: childhood period

Associated syndromes

Bardet-Biedl syndrome
Beckwith Wiedemann syndrome
CHARGE syndrome
fetal alcohol syndrome
Meckel Gruber syndrome: dominant feature
Miller Dieker syndrome
MURCS association: dominant feature
Noonan syndrome
Roberts syndrome
trisomy 13
VACTERL association: dominant feature

References

Incoming Links

Promoted articles (advertising)

{"current_user":null,"inclusions":[{"imageId":1391705,"studyId":14980,"caseSlug":"congenital-hypoplastic-kidney","caption":"Case 1: congenital renal hypoplasia - on right","isStack":true,"diagnosticCertainty":"confirmed_unsubstantiated","thumbnail":"https://prod-images-static.radiopaedia.org/images/1391705/0c23c753b0107267bfa92cbb3be3e5_big_gallery.jpg"},{"imageId":134023,"studyId":8340,"caseSlug":"unilateral-renal-agenesis-1","caption":"Case 2: unilateral right renal agenesis ","isStack":true,"diagnosticCertainty":"probable","thumbnail":"https://prod-images-static.radiopaedia.org/images/134023/06a38efd23a50daf649d9aaee9e57c_big_gallery.jpg"},{"imageId":557620,"studyId":11491,"caseSlug":"horseshoe-kidney-3","caption":"Case 3: horseshoe kidney","isStack":true,"diagnosticCertainty":"confirmed_substantiated","thumbnail":"https://prod-images-static.radiopaedia.org/images/557620/32ec7f0bf2e32c9b967a55443f9de4_big_gallery.jpg"},{"imageId":447086,"studyId":10268,"caseSlug":"multicystic-dysplastic-kidney","caption":"Case 4: multicystic dysplastic kidney","isStack":false,"diagnosticCertainty":"confirmed_unsubstantiated","thumbnail":"https://prod-images-static.radiopaedia.org/images/447086/fd00049058ee9c3f94eaff5e30fe55_big_gallery.jpg"},{"imageId":565226,"studyId":11589,"caseSlug":"autosomal-recessive-polycystic-kidney-disease-2","caption":" Case 5: ARPKD","isStack":false,"diagnosticCertainty":"confirmed_unsubstantiated","thumbnail":"https://prod-images-static.radiopaedia.org/images/565226/6d8a89baaa962dba9ef8f6e56a79a0_big_gallery.jpg"},{"imageId":630904,"studyId":12913,"caseSlug":"pelviureteric-junction-obstruction-puj","caption":"Case 6: PUJ obstruction","isStack":true,"diagnosticCertainty":"confirmed_substantiated","thumbnail":"https://prod-images-static.radiopaedia.org/images/630904/77d7a6b4a88a2eef350dc0bde46c84_big_gallery.jpg"},{"imageId":6154564,"studyId":28333,"caseSlug":"pelvic-kidney-2","caption":"Case 7","isStack":true,"diagnosticCertainty":"confirmed_substantiated","thumbnail":"https://prod-images-static.radiopaedia.org/images/6154564/da099e5551f86341ca431978317ae0efb7648e4ec3af6565d622a21f207630db_big_gallery.jpeg"},{"imageId":51690168,"studyId":82308,"caseSlug":"duplex-kidney-with-triple-renal-arteries","caption":"Case 8: Right duplex malrotated kidney with triple arterial supply","isStack":true,"diagnosticCertainty":"confirmed_unsubstantiated","thumbnail":"https://prod-images-static.radiopaedia.org/images/51690168/a4626afc6b88c6a27a7108a938b477_big_gallery.jpeg"},{"imageId":60425130,"studyId":129562,"caseSlug":"unilateral-renal-agenesis-2","caption":"Case 9: unilateral renal agenesis","isStack":false,"diagnosticCertainty":"confirmed_substantiated","thumbnail":"https://prod-images-static.radiopaedia.org/images/60425130/77fc67baa51604cc31389e79178f2023c9261323e9618dca5539b9a879a09e73_big_gallery.jpeg"}],"ddx_inclusions":[],"lang":"us"}

Updating… Please wait.

Unable to process the form. Check for errors and try again.

Thank you for updating your details.

Congenital renal anomalies

Citation, DOI, disclosures and article data

Associated syndromes

See also

References

Incoming Links

Promoted articles (advertising)

Articles

By Section:

By System:

Cases

Radiopaedia.org