Cruveilhier Baumgarten syndrome

Last revised by David Luong on 9 Jun 2023

The term Cruveilhier Baumgarten syndrome is attributed to cases of portal hypertension wherein a loud venous murmur can be detected over the upper abdomen. Cruveilhier Baumgarten disease is reserved for cases with congenital patency of the umbilical vein, congenital hypoplasia of the liver and portal system, and venous murmur heard over the umbilical vein 1.

On CT, Cruveilhier-Baumgarten syndrome is diagnosed by the presence of dilated tortuous paraumbilical veins in patients with cirrhosis. These veins originate from the left portal vein branch and traverse along the falciform ligament towards the umbilicus, forming a network of dilated periumbilical veins giving a ‘caput medusae’ appearance 2.

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