Cyanotic congenital heart disease
Citation, DOI, disclosures and article data
Citation:
Gaillard F, Knipe H, Rock P, et al. Cyanotic congenital heart disease. Reference article, Radiopaedia.org (Accessed on 07 Dec 2024) https://doi.org/10.53347/rID-8472
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rID:
8472
Article created:
Disclosures:
At the time the article was created Frank Gaillard had no recorded disclosures.
View Frank Gaillard's current disclosures
Last revised:
Disclosures:
At the time the article was last revised Henry Knipe had the following disclosures:
- Integral Diagnostics, Shareholder (ongoing)
- Micro-X Ltd, Shareholder (ongoing)
These were assessed during peer review and were determined to not be relevant to the changes that were made.
View Henry Knipe's current disclosures
Revisions:
9 times, by
7 contributors -
see full revision history and disclosures
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Synonyms:
- Cyanotic congenital heart diseases
- Cyanotic congenital heart defects
- Cyanotic congenital heart defect
A number of entities can present as cyanotic congenital heart disease. These can be divided into those with increased (pulmonary plethora) or decreased pulmonary vascularity:
-
increased pulmonary vascularity
- total anomalous pulmonary venous return (TAPVR) (types I and II)
- transposition of the great arteries (TGA)
- truncus arteriosus (types I, II, and III)
- large AVSD
- single ventricle without pulmonary stenosis
-
decreased pulmonary vascularity
- tetralogy of Fallot
-
hypoplastic right heart syndrome: pulmonary vascularity dependent on systemic collaterals
- tricuspid atresia
- hypoplastic right ventricle
- pulmonary atresia or severe stenosis
- Ebstein anomaly with atrial septal defect
- many other combined and infrequent anomalies such as
- double outlet right ventricle (DORV) with pulmonary stenosis
- single ventricle with pulmonary stenosis
- Uhl anomaly
- pentalogy of Cantrell
The most important cyanotic congenital heart defects can be remembered with the five Ts mnemonic.
Quiz questions
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References
- 1. Maurice M. Reeder. Reeder and Felson’s Gamuts in Radiology. (2003) ISBN: 9780387955889 - Google Books
- 2. William E. Brant, Clyde A. Helms. Fundamentals of Diagnostic Radiology. (2007) ISBN: 9780781761352 - Google Books
Incoming Links
Articles:
- Truncus arteriosus
- Rastelli procedure
- Prostaglandin-induced cortical hyperostosis in infants with cyanotic congenital heart disease
- Tricuspid atresia
- Tetralogy of Fallot
- Overriding aorta
- Congenital heart disease in echocardiography (an approach)
- Transposition of the great arteries
- Small for dates fetus
- Heterotaxy syndrome
- Asplenia syndrome
- Finger clubbing (mnemonic)
- Ebstein anomaly
- Right-sided aortic arch
- Congenital cardiovascular anomalies
- Hypoplastic left heart syndrome
- Acyanotic congenital heart disease
- Total anomalous pulmonary venous return
- Finger clubbing
- Pectus carinatum
Cases:
- Scimitar syndrome
- Finger clubbing - cyanotic heart disease (MRI)
- Hypoplastic left heart syndrome
- Truncus arteriosus - Van Praagh type A3
- Transposition of great vessels
- Transposition of the great arteries
- Total anomalous pulmonary venous return
- Tetralogy of Fallot
- Infracardiac total anomalous pulmonary venous return
Multiple choice questions:
Related articles: Pathology: Vascular: Congenital heart disease
There is more than one way to present the variety of congenital heart diseases. Whichever way they are categorized, it is helpful to have a working understanding of normal and fetal circulation, as well as an understanding of the segmental approach to imaging in congenital heart disease.
-
congenital heart disease
- subtypes
- normal relationship between chambers and valves
- shunting
- stenosis
- atrioventricular valves
- outflow tract
- great vessels
- venous inflow
- hypoplasia
- anomalous valves
- abnormal relationship of chambers and valves
- atrioventricular abnormality
- when associated with a univentricular heart
- atrioventricular discordance
- great vessel connection abnormality
- atrioventricular abnormality
- congenital heart disease - chest x-ray approach
-
surgical repairs (mnemonic)
- arterial switch procedure
- Blalock-Taussig shunt
- double switch procedure
- Fontan procedure
- Glenn procedure
- Mustard repair
- Norwood procedure
- Pott shunt
- pulmonary artery banding
- Rastelli procedure
- Sano shunt
- Senning repair
- total repair of tetralogy of Fallot (TOF)
- unifocalisation procedure
- Waterston shunt
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