Desmoplastic infantile tumour

Desmoplastic infantile tumours  are rare benign lesions that has aggressive radiological and pathological features. Patients usually present in first two years of life.

Stereotypical presentation:

  • increasing head circumference
  • bulging fontanelle
  • paresis
  • seizures
Histologic forms
CT Brain
  • large peripheral suptratentorial lesion demonstrating meningeal contact
  • oedema may be absent to moderate
  • heterogeneous mixed solid and cystic lesion; solid portion enhances and is usually superficial
  • enhancement and thickening of meninges may be present
  • may have adjacent remodeling of the calvarium
  • 50% demonstrate calcification

Overall, there is a favourable prognosis.

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Article Information

rID: 5588
Synonyms or Alternate Spellings:
  • Desmoplastic infantile tumor

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