Desmoplastic infantile tumours are rare benign lesions that has aggressive radiological and pathological features. Patients usually present in first two years of life.
- increasing head circumference
- bulging fontanelle
- large peripheral suptratentorial lesion demonstrating meningeal contact
- oedema may be absent to moderate
- heterogeneous mixed solid and cystic lesion; solid portion enhances and is usually superficial
- enhancement and thickening of meninges may be present
- may have adjacent remodeling of the calvarium
- 50% demonstrate calcification
Overall, there is a favourable prognosis.
- 1. Guillaume Trehan, Helene Brugea, Matthieu Vinchob, Chadi Khalil, Marie M. Ruchoux, Patrick Dhellemmes and Gustavo Soto Are. MR Imaging in the Diagnosis of Desmoplastic Infantile Tumor: Retrospective Study of Six Cases. American Journal of Neuroradiology 25:1028-1033, June-July 2004