Desmoplastic small round cell tumor of the pleura
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At the time the article was created Yuranga Weerakkody had no recorded disclosures.View Yuranga Weerakkody's current disclosures
At the time the article was last revised Sally Ayesa had no recorded disclosures.View Sally Ayesa's current disclosures
Tend to occur in younger patients (mean ~ 25.5 years) and with a slightly greater male predilection.
Treatment and prognosis
DSRCT tend to be aggressive tumors with a poor prognosis.
History and etymology
DSRCT was first described in 1989 by Gerald and Rosai and Ordonez et al. as a highly aggressive and rare mesenchymal tumor arising from serosal surfaces.
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