Doege-Potter syndrome
Last revised by Daniel J Bell on 2 Jul 2022
Citation, DOI, disclosures and article data
Citation:
Wanderley M, Bell D, Gaillard F, et al. Doege-Potter syndrome. Reference article, Radiopaedia.org (Accessed on 25 Apr 2024) https://doi.org/10.53347/rID-57849
Permalink:
rID:
57849
Article created:
16 Jan 2018,
Mark Wanderley ◉
Disclosures:
At the time the article was created Mark Wanderley had no recorded disclosures.
View Mark Wanderley's current disclosures
Last revised:
2 Jul 2022,
Daniel J Bell ◉
Disclosures:
At the time the article was last revised Daniel J Bell had no financial relationships to ineligible companies to disclose.
View Daniel J Bell's current disclosures
Revisions:
5 times, by
5 contributors -
see full revision history and disclosures
Systems:
Sections:
Synonyms:
- Doege Potter syndrome
- Non-islet cell tumour hypoglycaemia (NICTH)
- Non-islet cell tumour hypoglycemia (NICTH)
Doege-Potter syndrome is a paraneoplastic non-islet cell tumour hypoglycaemia, secondary to a solitary fibrous tumour, most commonly pulmonary, secreting insulin-like growth factor-2 (IGF-2).
It is rare and more often found with higher grade solitary fibrous tumours 1-4.
References
- 1. Ahluwalia N, Attia R, Green A, Cane P, Routledge T. Doege-Potter Syndrome. Ann R Coll Surg Engl. 2015;97(7):e105-7. doi:10.1308/rcsann.2015.0023 - Pubmed
- 2. Han G, Zhang Z, Shen X et al. Doege-Potter Syndrome: A Review of the Literature Including a New Case Report. Medicine (Baltimore). 2017;96(27):e7417. doi:10.1097/MD.0000000000007417 - Pubmed
- 3. Chamberlain M & Taggart D. Solitary Fibrous Tumor Associated with Hypoglycemia: An Example of the Doege-Potter Syndrome. J Thorac Cardiovasc Surg. 2000;119(1):185-7. doi:10.1016/s0022-5223(00)70242-x - Pubmed
- 4. Tariq M, Din N, Abdul-Ghafar J, Park Y. The Many Faces of Solitary Fibrous Tumor; Diversity of Histological Features, Differential Diagnosis and Role of Molecular Studies and Surrogate Markers in Avoiding Misdiagnosis and Predicting the Behavior. Diagn Pathol. 2021;16(1):32. doi:10.1186/s13000-021-01095-2 - Pubmed
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