Dorsal dermal sinus is caused by incomplete separation of the superficial ectoderm from the neural ectoderm, resulting in a focal segmental adhesion.
Later during embryogenesis, the spinal cord ascends relative to the spinal canal and stretches the adhesion into a long, tubular tract.
Dorsal dermal sinus manifests as a small dimple or pinpoint ostium, which is often associated with an area of hyperpigmented, angiomatous skin or hypertrichosis and occurs in a midline location or rarely in a paramedian location.
Soft-tissue asymmetry and bone anomalies are common findings.
Predominantly located in the lumbosacral region and less often in the occipital region.
- ultrasound can show the entire length of the tract from the skin to the spinal cord
- the tract can be difficult to identify within the subcutaneous fat
- the tract is clearly demonstrated in the anechoic, cerebrospinal fluid–filled subarachnoid space as an echogenic structure
Treatment and prognosis
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- 3. Surgery of the Pediatric Spine. Thieme. ISBN:1588903427. Read it at Google Books - Find it at Amazon