Double outlet left ventricle (DOLV) is an extremely rare congenital cardiac anomaly where both the aorta and pulmonary trunk arise from the anatomical left ventricle. It is usually classified as a conotruncal anomaly and is often associated with a ventricular septal defect with normal continuity between the aortic valve and anterior mitral valve.
- ventricular septal defect
- subpulmonic and subaortic obstruction
Chest radiographic features relate to the presence or absence of pulmonic valvular stenosis.
- in the presence of pulmonic stenosis, findings are similar to tetralogy of Fallot with a normal heart size and decreased pulmonary flow.
- without pulmonic stenosis, moderate cardiomegaly and increased pulmonary blood flow are evident.
It demonstrates the abnormal origin of the pulmonary artery from the left ventricle, normal aortic-mitral continuity, and VSD.
It will demonstrate:
- abnormal origin of the pulmonary artery from the left ventricle,
- VSD defect, and
- aortic-anterior mitral valve leaflet continuity
In the absence of pulmonic stenosis consider:
Congenital heart disease
There is more than one way to present the variety of congenital heart diseases. Whichever way they are categorised, it is helpful to have a working understanding of normal and fetal circulation, as well as an understanding of the segmental approach to imaging in congenital heart disease.
congenital heart disease
- normal relationship between chambers and valves
- atrioventricular valves
- outflow tract
- great vessels
- venous inflow
- anomalous valves
- abnormal relationship of chambers and valves
- atrioventricular abnormality
- great vessel connection abnormality
- conotruncal cardiac anomalies
- pentalogy of Cantrell
- Shone syndrome
- congenital heart disease - chest x-ray approach
surgical repairs (mnemonic)
- arterial switch procedure
- Blalock-Taussig shunt
- double switch procedure
- Fontan procedure
- Glenn procedure
- Mustard repair
- Norwood procedure
- Pott shunt
- pulmonary artery banding
- Rastelli procedure
- Sano shunt
- Senning repair
- total repair of tetralogy of Fallot (TOF)
- unifocalisation procedure
- Waterston shunt