Eosinophilic fasciitis

Eosinophilic fasciitis (EF), also known as Shulman syndrome, is an uncommon connective tissue disorder.

It can potentially present at age. There is a recognized female predilection 3,4.

Patients typically present with pronounced extremity edema and skin induration. 

Clinical features include

Eosinophilic fasciitis tends to involve the limbs.

Tends to demonstrate muscular fascial plane thickening without any myositis. Changes are generally symmetrical. Signal changes include 1,3:

  • T2 FS/STIR: high signal compared to muscle involving fascial planes
  • T1 C+ (Gd): shows fascicle enhancement

Tends to respond to corticosteroids with excellent response.

First described by L E Shulman et al. in 1975 2.

Imaging differential considerations include:

  • necrotizing fasciitis: tends to have accompanying fluid/gas collections/abscess formation, cellulitis and muscle inflammation
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Article information

rID: 10777
Tag: cases, cases
Synonyms or Alternate Spellings:
  • Shulman syndrome
  • Shulman's syndrome

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Cases and figures

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  • Case 2
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