Granulomatosis with polyangiitis (CNS manifestations)

CNS manifestations of granulomatosis with polyangiitis (GPA) (previously known as Wegener's granulomatosis) are rare. Granulomatosis with polyangiitis (Wegener granulomatosis), is a multi-system systemic necrotizing non-caseating granulomatous vasculitis affecting small to medium-sized arteries, capillaries and veins.

Epidemiology

CNS manifestations of GPA occur only in ~5% (range 2-9%) of the patients 1,2.

Pathology

GPA manifests in the CNS as 1,2:

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Article information

rID: 40104
Section: Syndromes
Synonyms or Alternate Spellings:
  • Wegner granulomatosis: CNS manifestations

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Cases and figures

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    Case 1: meningeal granulomatosis
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