Haemangiopericytomas of the spleen are very rare vascular neoplasm with only a few case reports available at the time of writing.
Splenic haemangiopericytomas are typically asymptomatic or can result in splenomegaly.
These are soft tissue vascular neoplasms arising from capillary pericytes 1. It is often characterised as having variable biologic behaviour, but it is regarded as a tumour that may have very high malignant potential 3.
Since the tumours are very rare, with only occasional case reports describing the imaging findings.
- a large splenic mass with polylobular contours
- smaller disseminated lesions throughout the spleen 3
Speckled calcification may be seen on CT scans, and contrast-enhanced studies may show discrete hyperattenuation of solid portions and septation.
History and etymology
It was first reported by Guadalajara Jurado et al. in 1989 4.
- 1. Kumar M, Tripathi K, Khanna R et-al. Hemangiopericytoma of the spleen: unusual presentation as multiple abscess. World J Surg Oncol. 2005;3 : 77. doi:10.1186/1477-7819-3-77 - Free text at pubmed - Pubmed citation
- 2. Ciftci AO, Gedikoğlu G, Firat PA et-al. Childhood splenic hemangiopericytoma: a previously unreported entity. J. Pediatr. Surg. 1999;34 (12): 1884-6. J. Pediatr. Surg. (link) - Pubmed citation
- 3. Abbott RM, Levy AD, Aguilera NS et-al. From the archives of the AFIP: primary vascular neoplasms of the spleen: radiologic-pathologic correlation. Radiographics. 24 (4): 1137-63. doi:10.1148/rg.244045006 - Pubmed citation
- 4. Guadalajara jurado J, Turégano fuentes F, García menendez C et-al. Hemangiopericytoma of the spleen. Surgery. 1989;106 (3): 575-7. - Pubmed citation
- 5. Neill JS, Park HK. Hemangiopericytoma of the spleen. Am. J. Clin. Pathol. 1991;95 (5): 680-3. - Pubmed citation
- 6. Ferrozzi F, Bova D, Draghi F et-al. CT findings in primary vascular tumors of the spleen. AJR Am J Roentgenol. 1996;166 (5): 1097-101. AJR Am J Roentgenol (citation) - Pubmed citation
- normal appearance of the spleen
- pseudolesion of the spleen: inhomogeneous splenic enhancement
splenic lesions and anomalies
- congenital anomalies
- mass lesions
- infiltrative processes
- incidental splenic lesion (approach)