Revision 6 for 'Hemangiopericytoma of the spleen'

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Hemangiopericytoma of the spleen

Hemangiopericytomas of the spleen are a very rare vascular neoplasm with only a few case reports available at the time of writing.

Clinical presentation

Splenic hemangiopericytomas are typically asymptomatic or can result in splenomegaly.

Pathology

These are a soft tissue vascular neoplasm arising from capillary pericytes 1. It is often characterized as having variable biologic behavior, but it is regarded as a tumor that may have very high malignant potential 3.

Radiographic features

Since the tumors are very rare, with only occasional case reports describing the imaging findings.

CT
  • a large splenic mass with polylobular contours
    or
  • smaller disseminated lesions throughout the spleen 3

Speckled calcification may be seen on CT scans, and contrast-enhanced studies may show discrete hyperattenuation of solid portions and septation.

History and etymology

It was first reported by Guadalajara Jurado et al in 1989 4.

See also

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