Harlequin eye deformity

Last revised by Daniel J Bell ◉ on 4 Jan 2022

Citation, DOI, disclosures and article data

Citation:

Sargent M, Bell D, Saber M, et al. Harlequin eye deformity. Reference article, Radiopaedia.org (Accessed on 23 Mar 2023) https://doi.org/10.53347/rID-5906

DOI:

https://doi.org/10.53347/rID-5906

Permalink:

https://radiopaedia.org/articles/5906

rID:

5906

Article created:

27 Mar 2009, Michael Sargent

Disclosures:

At the time the article was created Michael Sargent had no recorded disclosures.

View Michael Sargent's current disclosures

Last revised:

4 Jan 2022, Daniel J Bell ◉

Disclosures:

At the time the article was last revised Daniel J Bell had no recorded disclosures.

View Daniel J Bell's current disclosures

Revisions:

14 times, by 6 contributors - see full revision history and disclosures

Systems:

Central Nervous System, Musculoskeletal, Paediatrics, Head & Neck

Sections:

Signs

Tags:

refs

The harlequin eye deformity is characterized by elevation of the superolateral corner of the orbit. It may be seen in unilateral (plagiocephaly) or bilateral (brachycephaly) coronal suture synostosis.

History and etymology

The term harlequin eye derives from the appearance of the eyes on a harlequin mask with their exaggerated superior orbital margins. This was supposed to suggest a quizzical expression.