Hereditary renal cancer syndromes
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Despite the vast majority of renal cancers being sporadic, there are a number of hereditary renal cancer syndromes:
- von Hippel Lindau syndrome: predominantly clear cell type
- tuberous sclerosis: predominantly clear cell type
- hereditary leiomyomata renal cell cancer syndrome: described in ISUP Vancouver classification 3
- Birt-Hogg-Dube syndrome: predominantly chromophobe renal cell cancer (also associated with oncocytic adenomas)
- hereditary papillary renal cell cancer type 1: papillary type I
- hereditary non polyposis colon cancer (Lynch type II): predominantly transitional cell carcinoma of renal pelvis
- hereditary renal oncocytoma
- sickle cell anaemia: medullary renal carcinoma
See also
-<a title="hereditary leiomyomata renal cell cancer syndrome (HLRCC)" href="/articles/hereditary-leiomyomata-renal-cell-cancer-syndrome-hlrcc">hereditary leiomyomata renal cell cancer syndrome</a>: described in ISUP Vancouver classification <sup>3</sup>- +<a href="/articles/hereditary-leiomyomata-renal-cell-cancer-syndrome-hlrcc">hereditary leiomyomata renal cell cancer syndrome</a>: described in ISUP Vancouver classification <sup>3</sup>
-<a href="/articles/hereditary-non-polyposis-colorectal-cancer-1">hereditary non polyposis colon cancer</a> (Lynch type II): predominantly <a href="/articles/transitional-cell-carcinoma-of-the-renal-pelvis">transitional cell carcinoma of renal pelvis</a>- +<a href="/articles/hereditary-non-polyposis-colorectal-cancer-1">hereditary non polyposis colon cancer</a> (Lynch type II): predominantly <a href="/articles/transitional-cell-carcinoma-renal-pelvis">transitional cell carcinoma of renal pelvis</a>
-</ul><h4>See also</h4><ul><li><a title="Renal cell carcinoma" href="/articles/renal-cell-carcinoma-1">renal cell carcinoma</a></li></ul>- +<li>
- +<a title="Sickle cell anaemia" href="/articles/sickle-cell-disease">sickle cell anaemia</a>: <a title="Medullary carcinoma of the kidney" href="/articles/renal-medullary-carcinoma">medullary renal carcinoma</a>
- +</li>
- +</ul><h4>See also</h4><ul><li><a href="/articles/renal-cell-carcinoma-1">renal cell carcinoma</a></li></ul>