Hereditary renal cancer syndromes
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Despite the vast majority of renal cancers being sporadic, there are a number of hereditary renal cancer syndromes:
- von Hippel Lindau syndrome: predominantly clear cell type
- tuberous sclerosis: predominantly clear cell type
- hereditary leiomyomata renal cell cancer syndrome: described in ISUP Vancouver classification 3
- Birt-Hogg-Dube syndrome: predominantly chromophobe renal cell cancer (also associated with oncocytic adenomas)
- hereditary papillary renal cell cancer type 1: papillary type I
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hereditary non
polyposis-polyposis colon cancer (Lynch type II): predominantly transitional cell carcinoma of the renal pelvis - hereditary renal oncocytoma
- sickle cell anaemia: medullary renal carcinoma
See also
-<a href="/articles/birt-hogg-dube-syndrome-1">Birt-Hogg-Dube syndrome</a>: predominantly chromophobe renal cell cancer (also associated with <a href="/articles/renal-oncocytoma">oncocytic adenomas</a>)</li>- +<a href="/articles/folliculin-gene-associated-syndrome">Birt-Hogg-Dube syndrome</a>: predominantly chromophobe renal cell cancer (also associated with <a href="/articles/renal-oncocytoma">oncocytic adenomas</a>)</li>
-<a href="/articles/hereditary-non-polyposis-colorectal-cancer-1">hereditary non polyposis colon cancer</a> (Lynch type II): predominantly <a href="/articles/transitional-cell-carcinoma-renal-pelvis">transitional cell carcinoma of renal pelvis</a>- +<a href="/articles/hereditary-non-polyposis-colorectal-cancer-1">hereditary non-polyposis colon cancer</a> (Lynch type II): predominantly <a href="/articles/transitional-cell-carcinoma-renal-pelvis">transitional cell carcinoma of the renal pelvis</a>
-<a title="Sickle cell anaemia" href="/articles/sickle-cell-disease">sickle cell anaemia</a>: <a title="Medullary carcinoma of the kidney" href="/articles/renal-medullary-carcinoma">medullary renal carcinoma</a>- +<a href="/articles/sickle-cell-disease">sickle cell anaemia</a>: <a href="/articles/renal-medullary-carcinoma">medullary renal carcinoma</a>