Hereditary renal cancer syndromes
Updates to Article Attributes
Body
was changed:
Despite the vast majority of renal cancers being sporadic, there are a number of hereditary renal cancer syndromes:
- von Hippel Lindau syndrome: predominantly clear cell type
- tuberous sclerosis: predominantly clear cell type (also associated with angiomyolipoma)
- hereditary paraganglioma-pheochromocytoma syndromes: predominantly clear cell type
- hereditary papillary renal cell carcinoma: papillary type 1
- hereditary leiomyomatosis and renal cell carcinoma: predominantly papillary type 2
- Birt-Hogg-Dube syndrome: predominantly chromophobe type (also associated with oncocytoma and hybrid oncytic and clear cell carcinoma)
-
hereditary non-polyposis colon cancer (Lynch type II): predominantly upper tract
transitional cellurothelial carcinomaof the renal pelvis - sickle cell anaemia: renal medullary carcinoma
- hereditary renal oncocytoma: oncocytoma
See also
-<a title="hereditary paraganglioma-pheochromocytoma syndromes" href="/articles/hereditary-paraganglioma-pheochromocytoma-syndromes">hereditary paraganglioma-pheochromocytoma syndromes</a>: predominantly <a href="/articles/clear-cell-renal-cell-carcinoma">clear cell</a> type</li>- +<a href="/articles/hereditary-paraganglioma-pheochromocytoma-syndromes">hereditary paraganglioma-pheochromocytoma syndromes</a>: predominantly <a href="/articles/clear-cell-renal-cell-carcinoma">clear cell</a> type</li>
-<a href="/articles/hereditary-non-polyposis-colorectal-cancer-1">hereditary non-polyposis colon cancer</a> (Lynch type II): predominantly <a href="/articles/transitional-cell-carcinoma-renal-pelvis">transitional cell carcinoma of the renal pelvis</a>- +<a href="/articles/hereditary-non-polyposis-colorectal-cancer-1">hereditary non-polyposis colon cancer</a> (Lynch type II): predominantly upper tract <a href="/articles/transitional-cell-carcinoma-renal-pelvis">urothelial carcinoma</a>