Hereditary renal cancer syndromes
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Despite the vast majority of renal cancers being sporadic, there are a number of hereditary renal cancer syndromes:
- von Hippel Lindau syndrome: predominantly clear cell type
- tuberous sclerosis: predominantly clear cell type (also associated with angiomyolipoma)
- hereditary paraganglioma-pheochromocytoma syndromes: predominantly clear cell type
- hereditary papillary renal cell carcinoma: papillary type 1
- hereditary leiomyomatosis and renal cell carcinoma: predominantly papillary type 2
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Birt-Hogg
-Dube syndrome-Dubé syndrome: predominantly chromophobe type(also associated with, oncocytomaand, or a hybridoncytic and clear cell carcinoma)of both - hereditary non-polyposis colon cancer (Lynch type II): predominantly upper tract urothelial carcinoma
- sickle cell trait or hemoglobin SC disease: renal medullary carcinoma
- hereditary renal oncocytoma: oncocytoma
See also
-<a href="/articles/folliculin-gene-associated-syndrome">Birt-Hogg-Dube syndrome</a>: predominantly <a href="/articles/chromophobe-renal-cell-carcinoma">chromophobe</a> type (also associated with <a href="/articles/renal-oncocytoma">oncocytoma</a> and hybrid oncytic and clear cell carcinoma)</li>- +<a href="/articles/birt-hogg-dube-syndrome-5">Birt-Hogg-Dubé syndrome</a>: predominantly <a href="/articles/chromophobe-renal-cell-carcinoma">chromophobe</a> type, <a href="/articles/renal-oncocytoma">oncocytoma</a>, or a hybrid of both</li>