Idiopathic aortitis is a rare form of non-infective aortitis with a lack of any known systemic disease.
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Epidemiology
There may be a greater predilection in females 1.
Clinical presentation
While many patients can be asymptomatic, it may present with symptoms of aortic inflammation such as back pain, abdominal pain and/or elevated inflammatory markers.
Pathology
It is characterized by giant cell or lymphoplasmacytic inflammation of the aorta without a secondary cause.
Location
Both the thoracic and abdominal aorta can be involved. When associated with an idiopathic inflammatory aneurysm, there tends to be involvement of the thoracic aorta.
Radiographic features
CT
Some authors suggest aneurysms associated with idiopathic aortitis have significantly larger and more diffuse dilatation of the thoracic aorta than patients with noninflammatory aneurysms 4.
Complications
Formation of inflammatory aortic aneurysms in the thoracic aorta or abdominal aorta.