Idiopathic aortitis

Last revised by David Luong on 15 Nov 2021

Idiopathic aortitis is a rare form of non-infective aortitis with a lack of any known systemic disease.

There may be a greater predilection in females 1.

While many patients can be asymptomatic, it may present with symptoms of aortic inflammation such as back pain, abdominal pain and/or elevated inflammatory markers.

It is characterized by giant cell or lymphoplasmacytic inflammation of the aorta without a secondary cause.

Both the thoracic and abdominal aorta can be involved. When associated with an idiopathic inflammatory aneurysm, there tends to be involvement of the thoracic aorta.

Some authors suggest aneurysms associated with idiopathic aortitis have significantly larger and more diffuse dilatation of the thoracic aorta than patients with noninflammatory aneurysms 4.

Formation of inflammatory aortic aneurysms in the thoracic aorta or abdominal aorta.

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