IgG-4 related lung disease

IgG-4 related lung disease is a recently described condition. It may occur with or without systemic involvement. It is considered part of the spectrum of IgG-4 related sclerosing disease.

Radiographic features

CT

On HRCT of the chest, it may be categorised into four major subtypes 5:

  1. solid nodular type
  2. round-shaped ground-glass opacities: showing multiple round-shaped ground glass opacities
  3. alveolar interstitial type: showing honeycombing, bronchiectasis and diffuse ground glass opacity
  4. bronchovascular type: showing thickening of bronchovascular bundles and interlobular septae
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Article Information

rID: 29369
System: Chest
Section: Pathology
Tag: cases
Synonyms or Alternate Spellings:
  • IgG-4 related interstitial lung disease
  • IgG4 related lung disease
  • IgG-4 related interstitial lung disease

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