Infantile fibrosarcoma of the lung

Last revised by Francis Deng on 2 Aug 2021

Infantile fibrosarcoma of the lung, also known as primary bronchopulmonary fibrosarcoma, is a very rare spindle-cell tumor.


More than 80% of cases are reported to occur within the 1st year of life. There is a slight predominance in male infants 1,2.

Clinical presentation

Patients may present with respiratory symptoms, fever, anemia and hypoglycemia.

Radiographic features

The imaging features of infantile fibrosarcoma, specifically in the lung, have not been described. However, extrapulmonary tumors on MRI tend to be hyperintense on T1 and T2 weighted sequences and demonstrate heterogeneous enhancement associated with tumoral hemorrhage 3.

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