Citation, DOI, disclosures and article data
Citation:
Weerakkody Y, Luong D, Bell D, Interstitial lung disease associated with primary biliary cholangitis. Reference article, Radiopaedia.org (Accessed on 13 Mar 2025) https://doi.org/10.53347/rID-94748
Interstitial lung disease associated with primary biliary cholangitis can occur in a variable pattern that can include 1:
Epidemiology
It may occur in approximately 15% of patients with primary biliary cholangitis 2.
There may be a higher predilection in older patients and in those with an elevated erythrocyte sedimentation rate (ESR). Concomitant presence of Sjögren syndrome can considerably increase the risk of interstitial lung disease.
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1. Koksal D, Koksal A, Gurakar A. Pulmonary Manifestations Among Patients with Primary Biliary Cirrhosis. J Clin Transl Hepatol. 2016;4(3):258-62. doi:10.14218/JCTH.2016.00024 - Pubmed
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2. Shen M, Zhang F, Zhang X. Primary Biliary Cirrhosis Complicated with Interstitial Lung Disease: A Prospective Study in 178 Patients. J Clin Gastroenterol. 2009;43(7):676-9. doi:10.1097/MCG.0b013e31818aa11e - Pubmed
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3. Victoria Sholomova, Larisa Akulkina, Michael Brovko et al. Lung Involvement in Primary Biliary Cholangitis (PBC). European Respiratory Journal. 2020;56(suppl 64). doi:10.1183/13993003.congress-2020.3397
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4. Bartosiewicz M, Siemion-Szcześniak I, Jędrych M et al. [Interstitial Lung Disease in Patients with Primary Biliary Cirrhosis]. Pneumonol Alergol Pol. 2012;80(5):471-81. - Pubmed
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