Intravascular papillary endothelial hyperplasia
Updates to Article Attributes
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was changed:
Intravascular papillary endothelial hyperplasias, also known as Masson tumors, are rare non-neoplastic vascular proliferations.
Clinical presentation
Patients usually present with an enlarging soft tissue mass 1.
Pathology
The lesion is a reactive process characterized by endothelial cell proliferation in the setting of venous stasis commonly associated with thrombosis. The pure form consists of organized thrombus limited to the vascular lumen. The mixed form arises in the setting of a preexisting vascular lesion such as hemangioma.
Radiographic features
MRI
Lesions are most commonly located in subcutaneous soft tissues and associated with a visible origin vessel. They are usually small (<2 cm), well-defined, round or oval, and heterogeneous in signal 1-6.
- T1: iso- to slightly hyperintense, with nodular foci of high signal intensity
- T2: hyperintense peripherally, with nodular foci of low signal intensity
- T1 C+: peripheral/septal or central enhancement
Treatment and prognosis
The treatment is surgical resection. The pure form of intravascular papillary endothelial hyperplasia carries no risk of recurrence when completely resected.
Differential diagnosis
-<p><strong>Intravascular papillary endothelial hyperplasias</strong>, also known as <strong>Masson tumors</strong>, are rare non-neoplastic vascular proliferations.</p><h4>Clinical presentation</h4><p>Patients usually present with an enlarging soft tissue mass <sup>1</sup>.</p><h4>Pathology</h4><p>The lesion is a reactive process characterized by endothelial cell proliferation in the setting of venous stasis commonly associated with thrombosis. The pure form consists of organized thrombus limited to the vascular lumen. The mixed form arises in the setting of a preexisting vascular lesion such as hemangioma.</p><h4>Radiographic features</h4><h5>MRI</h5><p>Lesions are most commonly located in subcutaneous soft tissues and associated with a visible origin vessel. They are usually small (<2 cm), well-defined, round or oval, and heterogeneous. </p><ul>- +<p><strong>Intravascular papillary endothelial hyperplasias</strong>, also known as <strong>Masson tumors</strong>, are rare non-neoplastic vascular proliferations.</p><h4>Clinical presentation</h4><p>Patients usually present with an enlarging soft tissue mass <sup>1</sup>.</p><h4>Pathology</h4><p>The lesion is a reactive process characterized by endothelial cell proliferation in the setting of venous stasis commonly associated with thrombosis. The pure form consists of organized thrombus limited to the vascular lumen. The mixed form arises in the setting of a preexisting vascular lesion such as hemangioma.</p><h4>Radiographic features</h4><h5>MRI</h5><p>Lesions are most commonly located in subcutaneous soft tissues and associated with a visible origin vessel. They are usually small (<2 cm), well-defined, round or oval, and heterogeneous in signal <sup>1-6</sup>. </p><ul>
-</ul><h4>Treatment and prognosis</h4><p>The treatment is surgical resection. The pure form of intravascular papillary endothelial hyperplasia carries no risk of recurrence when completely resected.</p><h4>Differential diagnosis</h4><ul><li><a title="Angiosarcoma" href="/articles/angiosarcoma">angiosarcoma</a></li></ul><p> </p>- +</ul><h4>Treatment and prognosis</h4><p>The treatment is surgical resection. The pure form of intravascular papillary endothelial hyperplasia carries no risk of recurrence when completely resected.</p><h4>Differential diagnosis</h4><ul><li><a href="/articles/angiosarcoma">angiosarcoma</a></li></ul><p> </p>
References changed:
- 1. Craig KA, Escobar E, Inwards CY, Kransdorf MJ. Imaging characteristics of intravascular papillary endothelial hyperplasia. (2016) Skeletal radiology. 45 (11): 1467-72. <a href="https://doi.org/10.1007/s00256-016-2445-0">doi:10.1007/s00256-016-2445-0</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/27538971">Pubmed</a> <span class="ref_v4"></span>
- 2. Lee SJ, Choo HJ, Park JS, Park YM, Eun CK, Hong SH, Hwang JY, Lee IS, Lee J, Jung SJ. Imaging findings of intravascular papillary endothelial hyperplasia presenting in extremities: correlation with pathological findings. (2010) Skeletal radiology. 39 (8): 783-9. <a href="https://doi.org/10.1007/s00256-010-0888-2">doi:10.1007/s00256-010-0888-2</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/20157705">Pubmed</a> <span class="ref_v4"></span>
- 3. Kim OH, Kim YM, Choo HJ, Lee SJ, Kim YM, Yi JH, Lee YH. Subcutaneous intravascular papillary endothelial hyperplasia: ultrasound features and pathological correlation. (2016) Skeletal radiology. 45 (2): 227-33. <a href="https://doi.org/10.1007/s00256-015-2281-7">doi:10.1007/s00256-015-2281-7</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/26559670">Pubmed</a> <span class="ref_v4"></span>
- 4. Sung J, Kim JY, Yoo C. Intravascular papillary endothelial hyperplasia: magnetic resonance imaging of finger lesions. (2016) Skeletal radiology. 45 (2): 235-42. <a href="https://doi.org/10.1007/s00256-015-2296-0">doi:10.1007/s00256-015-2296-0</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/26603891">Pubmed</a> <span class="ref_v4"></span>
- 5. Lee SH, Suh JS, Lim BI, Yang WI, Shin KH. Intravascular papillary endothelial hyperplasia of the extremities: MR imaging findings with pathologic correlation. (2004) European radiology. 14 (5): 822-6. <a href="https://doi.org/10.1007/s00330-003-2190-3">doi:10.1007/s00330-003-2190-3</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/14689228">Pubmed</a> <span class="ref_v4"></span>
Systems changed:
- Musculoskeletal