Intraventricular meningioma

Changed by Frank Gaillard, 16 Jan 2016

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Intraventricular meningiomas are rare intracranial tumours that represent an uncommon subtype of the more classical classical extra-axialmeningioma and represent between 0.5 and 2% of all meningiomas. Despite its rarity, they represent one of the commonest adult intraventricular neoplasms 4.

Epidemiology

Most intraventricular meningiomas presentbetween the 4th and 6th decades3 with a recognised female predilection (M:F ratio of 1:2) 4.

Clinical presentation

Intraventricular meningiomas present usually due to mass effect, either by direct compression of the adjacent brain, or from obstruction to normal CSF drainage with resultanthydrocephalus

Pathology

Intraventricular meningiomas are thought to arise from mengingothelial inclusion bodies located in the tela choroidea and/or mesenchymal stroma of the choroid plexus  5. In general, these meningiomas are most commonly of the fibrous meningiomas variety 5

Location

They are most frequently (80%) seen at thetrigone of thelateral ventricles and for reasons that are not clear, slightly more frequently on the left. Considering the distribution of meningiomas, the intraventricular location is comparatively comparativelycommoner in children (20% ofpaediatric meningiomas)

Radiographic features

Their signal and attenuation characteristics are the same as other meningiomas, demonstrating essentially isodensity and intensity to grey matter precontrast and vivid, usually homogenous enhancement following administration of contrast. Compared to extra-axial meningiomas, a greater proportion are calcified (50% compared to 20% for standard meningioma).

For further discussion of the radiographic appearances of these tumours, refer to the general article: meningioma

Treatment and prognosis

As is the case with other meningiomas, provided complete excision is possible, surgical excision is curative and therefore the treatment of choice. 

Differential diagnosis

The differential somewhat depends on location and age of the patient, however in general considerations should include:

See also

  • -<p><strong>Intraventricular meningiomas</strong> are rare intracranial tumours that represent an uncommon subtype of the more classical extra-axial <a href="/articles/meningioma">meningioma</a> and represent between 0.5 and 2% of all meningiomas. Despite its rarity, they represent one of the commonest <a href="/articles/adult-intraventricular-neoplasms">adult intraventricular neoplasms</a> <sup>4</sup>.</p><h4>Epidemiology</h4><p>Most intraventricular meningiomas present<sup> </sup>between the 4<sup>th</sup> and 6<sup>th</sup> decades <sup>3</sup> with a recognised female predilection (M:F ratio of 1:2) <sup>4</sup>.</p><h4>Clinical presentation</h4><p>Intraventricular meningiomas present usually due to mass effect, either by direct compression of the adjacent brain, or from obstruction to normal CSF drainage with resultant <a href="/articles/obstructive-hydrocephalus">hydrocephalus</a>. </p><h4>Pathology</h4><p>Intraventricular meningiomas are thought to arise from <a href="/articles/mengingothelial-inclusion-bodies">mengingothelial inclusion bodies</a> located in the <a href="/articles/tela-choroidea">tela choroidea</a> and/or <a href="/articles/mesenchymal-stroma">mesenchymal stroma</a> of the <a href="/articles/choroid-plexus">choroid plexus</a>  <sup>5</sup>. In general, these meningiomas are most commonly of the <a href="/articles/fibroblastic-meningioma">fibroblastic</a> variety <sup>5</sup>. </p><h5>Location</h5><p>They are most frequently (80%) seen at the <a href="/articles/trigone">trigone</a> of the <a href="/articles/lateral-ventricles">lateral ventricles</a> and for reasons that are not clear, slightly more frequently on the left. Considering the distribution of meningiomas, the intraventricular location is comparatively<em> </em>commoner in children (20% of <a href="/articles/paediatric-meningiomas">paediatric meningiomas</a>)</p><ul>
  • -<li>80% trigone of <a href="/articles/lateral-ventricles">lateral ventricle</a>
  • +<p><strong>Intraventricular meningiomas</strong> are rare intracranial tumours that represent an uncommon subtype of the more classical extra-axial <a href="/articles/meningioma">meningioma</a> and represent between 0.5 and 2% of all meningiomas. Despite its rarity, they represent one of the commonest <a href="/articles/adult-intraventricular-neoplasms">adult intraventricular neoplasms</a> <sup>4</sup>.</p><h4>Epidemiology</h4><p>Most intraventricular meningiomas present<sup> </sup>between the 4<sup>th</sup> and 6<sup>th</sup> decades <sup>3</sup> with a recognised female predilection (M:F ratio of 1:2) <sup>4</sup>.</p><h4>Clinical presentation</h4><p>Intraventricular meningiomas present usually due to mass effect, either by direct compression of the adjacent brain, or from obstruction to normal CSF drainage with resultant <a href="/articles/obstructive-hydrocephalus">hydrocephalus</a>. </p><h4>Pathology</h4><p>Intraventricular meningiomas are thought to arise from <a href="/articles/mengingothelial-inclusion-bodies">mengingothelial inclusion bodies</a> located in the <a href="/articles/tela-choroidea">tela choroidea</a> and/or <a href="/articles/mesenchymal-stroma">mesenchymal stroma</a> of the <a href="/articles/choroid-plexus">choroid plexus</a>  <sup>5</sup>. In general, these meningiomas are most commonly of the <a title="Fibrous meningioma" href="/articles/fibrous-meningioma">fibrous meningiomas</a> <sup>5</sup>. </p><h5>Location</h5><p>They are most frequently (80%) seen at the <a href="/articles/trigone">trigone</a> of the <a href="/articles/lateral-ventricles">lateral ventricles</a> and for reasons that are not clear, slightly more frequently on the left. Considering the distribution of meningiomas, the intraventricular location is comparatively<em> </em>commoner in children (20% of <a href="/articles/paediatric-meningiomas">paediatric meningiomas</a>)</p><ul>
  • +<li>80% trigone of <a href="/articles/lateral-ventricles">lateral ventricle</a>
  • -<a title="Choroid plexus metastases" href="/articles/choroid-plexus-metastases">choroid plexus metastases</a><ul>
  • +<a href="/articles/choroid-plexus-metastases">choroid plexus metastases</a><ul>
  • -<li><a href="/articles/intraventricular-masses-an-approach">intraventricular masses-an approach</a></li>
  • +<li><a href="/articles/intraventricular-masses-an-approach-1">intraventricular masses-an approach</a></li>

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