Lie classification of vasculitis

The Lie classification of vasculitis was proposed in 1994 ¹. 

Classification

Primary vasculitides

• affecting large, medium, and small blood vessels (see large vessel vasculitides)
  • Takayasu arteritis
  • temporal arteritis (giant cell arteritis)
  • isolated angiitis of the central nervous system
  • Hughes-Stovin syndrome
• affecting medium and small blood vessels
  • polyarteritis nodosa (PAN)
  • eosinophilic granulomatosis with polyangiitis (formerly Churg-Strauss syndrome)
  • granulomatosis with polyangiitis (formerly Wegener granulomatosis)
• affecting small vessels
  • microscopic polyangiitis (microscopic polyarteritis)
  • IgA vasculitis (formerly Henoch-Schönlein purpura)
  • cutaneous leukocytoclastic angiitis
  • idiopathic, pauci-immune pulmonary capillaritis (IPIPC)
• miscellaneous conditions
  • Buerger disease (thromboangiitis obliterans)
  • Cogan syndrome
  • Kawasaki disease
  • Goodpasture syndrome
  • Behçet disease

Secondary vasculitides

• infection-related vasculitis
• vasculitis secondary to connective tissue disease, e.g. SLE, rheumatoid arthritis
• drug hypersensitivity related vasculitis
• vasculitis secondary to mixed essential cryoglobulinemia - cryoglobulinaemic vasculitis
• malignancy-related vasculitis (usually lymphoproliferative types)
• hypocomplementemic urticaria vasculitis
• post organ transplant vasculitis
• pseudovasculitic syndromes
  • myxoma
  • endocarditis
  • Sneddon syndrome

See also

• vasculitis
• Revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides