The Lie classification of vasculitis was proposed in 1994 1.
Classification
Primary vasculitides
- affecting large, medium, and small blood vessels (see large vessel vasculitides)
-
affecting medium and small blood vessels
- polyarteritis nodosa (PAN)
- eosinophilic granulomatosis with polyangiitis (formerly Churg-Strauss syndrome)
- granulomatosis with polyangiitis (formerly Wegener granulomatosis)
-
affecting small vessels
- microscopic polyangiitis (microscopic polyarteritis)
- IgA vasculitis (formerly Henoch-Schönlein purpura)
- cutaneous leukocytoclastic angiitis
- idiopathic, pauci-immune pulmonary capillaritis (IPIPC)
-
miscellaneous conditions
- Buerger disease (thromboangiitis obliterans)
- Cogan syndrome
- Kawasaki disease
- Goodpasture syndrome
- Behçet disease
Secondary vasculitides
- infection-related vasculitis
- vasculitis secondary to connective tissue disease, e.g. SLE, rheumatoid arthritis
- drug hypersensitivity related vasculitis
- vasculitis secondary to mixed essential cryoglobulinemia - cryoglobulinaemic vasculitis
- malignancy-related vasculitis (usually lymphoproliferative types)
- hypocomplementemic urticaria vasculitis
- post organ transplant vasculitis
- pseudovasculitic syndromes
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