Lipoblastoma of lung

Lipoblastoma of the lung is a fat derived thoracic tumour.

They occur during infancy and early childhood. More than 90% of cases are diagnosed in children less than 3 years of age, with nearly 75% occurring before the age of 12 months

Lipoblastomas are rare soft-tissue mesenchymal tumours principally derived of embryonic white fat 3. They typically occur in the extremities (70% of cases), with the remainder of cases in mediastinal, retroperitoneal, or paravertebral areas. Occurrence in the lung is rare. They can also involve the chest wall or pleura

They may be divided into two categories:

  • lipoblastoma: more common superficial well-defined mass
  • lipoblastomatosis: deep, unencapsulated infiltrative lesion 
Plain radiograph

Nonspecific findings - may be seen as a soft-tissue-opacity mass on plain radiographs.

CT

Seen as a fat containing lesion with predominant intratumoral stranding. 

MRI

Maybe useful in selected cases. A notable characteristic on MR imaging includes intratumoral streaks and whorls that correspond to the tumour’s fibrovascular network. Cystic changes can be seen. However, lipoblastomas lack the fluid or calcific components.  

On CT

  • myxoid liposarcomas may have a similar CT appearance but are relatively uncommon in children
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Article information

rID: 47138
Systems: Chest, Oncology
Section: Pathology
Tag: cases
Synonyms or Alternate Spellings:
  • Pulmonary lipoblastoma
  • Lipoblastoma of the lung
  • Pulmonary lipoblastomas

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