Luckenschadel skull, also known as lacunar skull or craniolacunae, is a dysplasia of the membranous skull vault and is associated with Chiari II malformations (seen in up to 80% of such cases). The inner table is more affected than the outer, with regions of apparent thinning (corresponding to nonossified fibrous bone) of the skull vault. If particularly severe, with the individual lacunae coalescing into larger defects the term craniofenestra is used.
The defect is not one of pressure from within (in contrast to copper beaten skull appearance of hydrocephalus, or normal convolutional markings) but rather of abnormal collagen development and ossification, since the skull vault ossification process is the membranous ossification.
The findings are usually seen on plain skull x-rays or CT.
Luckenschadel skull is characterised by groups of round, oval or finger shaped pits on the inner surface of the vault (membranous part), separated by ridges of bone. They lie in thickest part of frontal, parietal and upper occipital bone.
Treatment and prognosis
The condition is self limiting, typically resolving after 6 months of age.
Imaging differential considerations include
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