Citation, DOI, disclosures and article data
Citation:
Weerakkody Y, Knipe H, Lymphangiomatosis. Reference article, Radiopaedia.org (Accessed on 19 Apr 2024) https://doi.org/10.53347/rID-93397
Disclosures:
At the time the article was last revised Henry Knipe had the following disclosures:
- Integral Diagnostics, Shareholder (ongoing)
- Micro-X Ltd, Shareholder (ongoing)
These were assessed during peer review and were determined to
not be relevant to the changes that were made.
View Henry Knipe's current disclosures
Lymphangiomatosis is a rare mesenchymal disorder that is characterized by developmental "malformation" of multiple lymphatic channels (usually with dilatation).
Terminology
If lymphatic channels are purely dilated and not malformed the term lymphangiectasia is usually used. If lymphangiomatosis occurs in a singular localized form it is then the term lymphangioma can be used, and if it is widespread throughout the body then generalized lymphatic anomaly can be used.
Pathology
The condition can have various forms depending on organ involvement:
Associations
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1. Blei F. Lymphangiomatosis: Clinical Overview. Lymphatic Research and Biology. 2011;9(4):185-90. doi:10.1089/lrb.2011.0020
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2. Gordon K & Mortimer P. Progressive Lymphangiomatosis and Gorham's Disease: Case Report and Clinical Implications. Lymphatic Research and Biology. 2011;9(4):201-4. doi:10.1089/lrb.2011.0021
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3. Jin D, Sun X, Shen W, Zhao Q, Wang R. Diagnosis of Lymphangiomatosis: A Study Based on CT Lymphangiography. Academic Radiology. 2020;27(2):219-26. doi:10.1016/j.acra.2019.03.024
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