Question 3090
{"accessible":false,"alternatives":[{"id":14997,"text":"Birt-Hogg-Dubé syndrome "},{"id":14996,"text":"Langerhans cell histiocytosis (LCH) "},{"id":14995,"text":"lymphangioleiomyomatosis (LAM)"},{"id":14998,"text":"lymphocytic interstitial pneumonitis (LIP) "}],"archived":false,"correctAlternativeId":14997,"explanation":"\u003cp\u003eBirt-Hogg-Dubé syndrome is a genetic disorder caused by mutations in the \u003cem\u003eFLCN\u003c/em\u003e gene. It is characterized by the presence of pulmonary cysts, renal tumors, and skin fibrofolliculomas.\u0026nbsp;\u003c/p\u003e","id":3090,"imageUrl":null,"imageAttribution":null,"imageAttributionCaseInfo":null,"firstQuestionPath":"/questions/3091","nextQuestionPath":"/articles/lymphoid-interstitial-pneumonia/questions/2373","relatedArticles":[{"id":1565,"title":"Langerhans cell histiocytosis","link":"/articles/langerhans-cell-histiocytosis?lang=us"},{"id":5018,"title":"Pulmonary Langerhans cell histiocytosis","link":"/articles/pulmonary-langerhans-cell-histiocytosis?lang=us"},{"id":7334,"title":"Lymphangioleiomyomatosis","link":"/articles/lymphangioleiomyomatosis-1?lang=us"},{"id":20054,"title":"Birt-Hogg-Dubé syndrome","link":"/articles/birt-hogg-dube-syndrome-5?lang=us"}],"alsoUsedIn":[{"id":2520,"kind":"Course","title":"Radiopaedia 2025 - Virtual Conference - page 2520","link":"https://radiopaedia.org/courses/radiopaedia-2025-virtual-conference/pages/2520"},{"id":2520,"kind":"Course","title":"2024 Virtual Conference Private Use - page 2520","link":"https://radiopaedia.org/courses/2024-virtual-conference-private-use/pages/2520"},{"id":2520,"kind":"Course","title":"Radiopaedia 2024 - Virtual Conference - page 2520","link":"https://radiopaedia.org/courses/radiopaedia-2024-virtual-conference/pages/2520"},{"id":2520,"kind":"Course","title":"2025 Virtual Conference Private Use - page 2520","link":"https://radiopaedia.org/courses/2025-virtual-conference-private-use/pages/2520"},{"id":2014,"kind":"Course","title":"2024 Virtual Conference Private Use - page 2014","link":"https://radiopaedia.org/courses/2024-virtual-conference-private-use/pages/2014"},{"id":406,"kind":"LiveSchedule","title":"406","link":"https://radiopaedia.org/admin/live_schedules/406"},{"id":380,"kind":"LiveSchedule","title":"380","link":"https://radiopaedia.org/admin/live_schedules/380"},{"id":376,"title":"r24 Chung Cystic lung diseases","kind":"Inclusion","link":"https://radiopaedia.org/admin/course_inclusions/376"}],"stem":"\u003cp\u003eWhich disease is characterized by the presence of cysts and renal tumors, and is associated with mutations in the \u003cem\u003eFLCN\u003c/em\u003e gene?\u003c/p\u003e","menuLinks":[{"text":"Report problem with question","url":"https://docs.google.com/forms/d/e/1FAIpQLSfO3soWYhOjJ7yErSysyCe5V4A1CqW7WK3rDA7MtAkecMGqNw/viewform?entry.1624461248\u0026entry.553583435=https://radiopaedia.org/questions/3090"}],"attemptsPercentages":[{"alternativeId":"14995","percentage":12},{"alternativeId":"14997","percentage":84},{"alternativeId":"14998","percentage":1},{"alternativeId":"14996","percentage":3}],"promptToLogin":false,"questionManager":false,"articleId":"lymphoid-interstitial-pneumonia"}